MYH14 and bile duct papillary neoplasm: MYH14 can lead to two different conditions: DFNA4 with progressive non syndromic hearing loss starting in the first or second decade of life and leading to severe to profound hearing loss in the fourth decade of life (Firstly described by Mirghomizadeh et al., 2002); or to IPN associated with myopathy, hoarseness, and hearing loss (Choi et al., 2011).