AMH and testicular agenesis: However, since male-typical differentiation of the genital tract and the development of the external genitalia are dependent on the production of anti-Müllerian hormone (AMH) and androgens, the testis must have been present at least up to the 16th week of gestation in these individuals.7 In some circumstances anorchia may occur secondary to a vascular event or testicular torsion.8 Bilateral congenital anorchia has a prevalence of approximately 1:20,000 males and unilateral congenital anorchia a prevalence of 1:6500 males.9