CD79A and dermatitis herpetiformis, familial: DH can be defined as a disease presenting with: (i) symmetrical polymorphic lesions involving typical areas such as the extensor aspects of the limbs and sacral region, (ii) a predominant neutrophilic infiltrate at the dermal papillae at histopathology, (iii) granular IgA deposits along the dermal-epidermal junction, (iv) an invariable association with CD, and (v) a response to a lifelong GFD (7).