Congenital generalized lipodystrophy (Berardinelli–Seip syndrome; AGPAT2, BSCL2, CAV1, PTRF)Mandibuloacral dysplasia (LMNA, ZMPSTE24)Familial partial lipodystrophy (CIDEC, LIPE, WRN, PCYT1A)Autoinflammatory lipodystrophy (JMP/CANDLE syndrome; PSMB8)CGL-like phenotypes (PPARG, FOS). The gene discussed is ZMPSTE24; the disease is proteosome-associated autoinflammatory syndrome.