This is comparable to the pooled prevalence of FXTAS in male cerebellar ataxia patients, which is 1.5% (16/1049), reported in a meta‐analysis of FMR1 premutation screening studies (Jacquemont, Leehey, Hagerman, Beckett, & Hagerman, 2006). Here, FMR1 is linked to fragile X-associated tremor/ataxia syndrome.