To date, 14 disease genes for MODY are identified; most of them are transcription factors MODY1 (HNF4A), MODY3 (HNF1A), MODY4 (PDX1), MODY5 (HNF1B), MODY6 (NEUROD1/BETA2), MODY7 (KLF11), MODY8 (CEL), MODY9 (PAX4), MODY11 (BLK), and MODY14 (APPL1). Here, HNF1B is linked to MODY.