In Krabbe disease, the deficit of the β-galactocerebrosidase enzyme (GALC, E.C. 3.2.1.46) causes the accumulation of the lysosphingolipid β-galactosylsphyngosine, which is also known as “psychosine”, and is a major degradative product of myelin sheet turnover [4,5]. This evidence concerns the gene GALC and Krabbe disease.