Examples are cardiomyopathy in organic acidurias (25 mg/kg/day with improvement in the cardiomyopathy) [65], glutaric acidemia type II (500 mg per day of CoQ10 along with riboflavin with improvement in strength, lactate, and creatine kinase levels) [59], ataxia oculomotor apraxia type 1 (200–600 mg with reported improvement in strength, ataxia, and cessation of seizures in one patient) [60], GLUT-1 deficiency (30 mg/kg/day with improvement in the ataxia and nystagmus) [66]. Here, SLC2A1 is linked to cerebellar ataxia.