He was treated withcyclophosphamide and bortezomib with resolution of his MM and improvement in renal function.8 In the first reported case of MM with AAV, Kapoulas et al described a72-year-old male with MM (monoclonal IgG lambda as opposed to the other casereports, which were all IgG kappa) who presented with renal failure due to AAV withpositive MPO antibodies (vs negativity for all the previous case reports and MPO andPR-3 positivity for our case). The gene discussed is MPO; the disease is Miyoshi myopathy.