Regarding the relative frequency of organic acidemias in our population, aninteresting observation was the high number of glutaric aciduria type I (59patients) and 3-hydroxy-3-methylglutaric aciduria (40 patients) detected in ourstudy, with a similar prevalence to the other most prevalent organic acidurias, suchas methylmalonic acidemia (due to mutase deficiency or various cobalamindeficiencies including CblC and Cbl A). Here, CBLC is linked to Organic aciduria.