Function of CDH23 has not yet been defined but it is hypothesized to be involved in cell-cell adhesion because of its similarity in structure with Epithelial Cadherin (E-Cadherin) which has role in homophilic cell-cell adhesion.14 Additionally, genetic variations in TH (OMIM: 191290) and EVC2 (OMIM: 607261) encoding Tyrosine Hydroxylase and EvC Ciliary Complex Subunit 2 respectively, have also been reported in deafness. Here, EVC2 is linked to deafness.