It does not manifest true neural differentiation and recently the term spindle cell predominant trichodiscoma (SCPT) has been used instead.<h4>Case presentation</h4>We present a case of a 40-year-old male with co-incidence of NFH and basal cell carcinoma (BCC) that the mesenchymal components of NFH were similar to SCPT but these components highly expressed S-100 protein. The gene discussed is NEFH; the disease is basal cell carcinoma.