LGMD R9 (former LGMD2I), caused by mutations in fukutin-related protein (FKRP), is characterized by MRI signal changes in adductor muscles and in posterior thigh and posterior thigh and calf muscles, whereas tibialis anterior is usually spared and often hypertrophied. This evidence concerns the gene FKRP and autosomal recessive limb-girdle muscular dystrophy type 2I.