Deafness, autosomal recessive 77 (DFNB77, MIM # 613079) is a typical example of rare NSHL, which is caused by deleterious variants within lipoxygenase homology domains 1 (LOXHD1) located at chromosome 18q21.1 (MIM #613072) [7]. The gene discussed is LOXHD1; the disease is nodular sclerosis classical Hodgkin lymphoma.