Cystic fibrosis (CF) is a lethal genetic disorder caused by deleterious mutations in the CF transmembrane conductance regulator (CFTR) protein (Gadsby et al., 2006), resulting in compromised mucociliary clearance, chronic bacterial infections, and subsequent progressive inflammatory lung damage (Donaldson and Boucher, 2003). Here, CFTR is linked to cystic fibrosis.