Studies in different populations have reported associations of KIR genes and KIR/HLA-I genotypes with SSc susceptibility: KIR2DS2+/2DL2- in Germany [9]; KIR2DS1+/2DS2- and 2DS1+/HLA-C2+ in Canada [10]; 2DS3+, 2DS2+HLA/-C1+, and 2DL2+/HLA-C1+ in Turkey [11]; and 3DL1+/HLA-Bw4Thr- in Iran [12]. Here, KIR3DL1 is linked to systemic sclerosis.