It has been reported that LMNA mutations can cause autosomal forms of Emery-Dreifuss muscular dystrophy (AD-EDMD) and limb-girdle muscular dystrophy type 1B (LGMD1B), which show clinical features of proximal dominant muscle weakness [9, 32]. This evidence concerns the gene LMNA and Emery-Dreifuss muscular dystrophy.