The expert consensus practice recommendations formulated in the International Symposium of Inherited Diseases of the Pancreas in 2007 describe potential subjects for surveillance as follows: (1) individuals with PJS or hereditary pancreatitis; (2) BRCA1, BRCA2 or CDKN2A mutation carriers with at least one affected first- or second-degree relative; (3) individuals with three or more affected first-degree, second-degree or third-degree relatives; and (4) individuals with two affected relatives including at least one FDR [73]. Here, CDKN2A is linked to Peutz-Jeghers syndrome.