NICCD usually present itself as neonatal cholestasis, and characterized by decreased alanine aminotransferase (ALT) to aspartic acid transaminase (AST) ratio, hypoglycemia, decreased albumin level, prothrombin time (PT) elongation, multiple amino acidemia, high levels of alpha-fetoprotein (AFP), and fatty liver [1, 9]. Here, GPT is linked to neonatal intrahepatic cholestasis due to citrin deficiency.