In the case of Pkp2, variants have been detected in idiopathic ventricular fibrillation and SCD (36, 37), possible catecholaminergic polymorphic ventricular tachycardia (38), HCM, DCM and left ventricular non-compaction (39–41). This evidence concerns the gene PKP2 and paroxysmal familial ventricular fibrillation.