The role of MRI, a largely used method of studying myopathies, is still not completely investigated in lipid myopathies but some papers have been published for specific myopathies, as neutral lipid storage disease (NLSD), MTP and Very-Long-Chain Acyl-CoA Dehydrogenase (VLCAD) [7,8,9,10]. Here, ACADL is linked to myopathy.