As in Very-Long-Chain acyl-CoA Dehydrogenase Deficiency (VLCADD), Long-Chain 3-hydroxyacyl-CoA Dehydrogenase Deficiency (LCHADD), Multiple Acyl-CoA Dehydrogenase Deficiency (MADD), or CACT deficiency, also in CPT2 deficiency urgent treatment should be meticulous as there is a high risk of serious complications. Here, EHHADH is linked to hyperinsulinemic hypoglycemia, familial, 4.