Besides the telomerase genes, TERT and TERC, multiple studies have identified genetic polymorphisms in the 11p15 region (MUC5B and TOLLIP) related to the risk of IPF [21,22,23], and the genotype of MUC5B and TOLLIP has been shown to be significantly associated with prognosis and therapeutic responses among IPF patients [24,25,26]. This evidence concerns the gene MUC5B and idiopathic interstitial pneumonia.