KCNJ11 and congenital isolated hyperinsulinism: Mutations in 11 genes (ABCC8, KCNJ11, GCK, GLUD1, HADH, PGM1, HNF1a, HNF4a, INSR, FOXA2, and CACNA1D) and the inappropriate expression of SLC16A1 and HK1 have been associated with CHI (19).