LAMA2-related muscular dystrophy is due to defect in the gene encoding the α2 subunit, which together with β1 and γ1 chains form laminin-211 (Lm-211), the most prevalent laminin found in basement membrane (BM), surrounding muscle fibers, and also in the Schwann cells of peripheral nerves [2]. The gene discussed is LAMA2; the disease is muscular dystrophy.