Episodic ataxia type 1 (EA1), a <i>Shaker</i>-like K<sup>+</sup><i>channelopathy</i>, is a consequence of genetic anomalies in the <i>KCNA1</i> gene that lead to dysfunctions in the voltage-gated K<sup>+</sup> channel Kv1. This evidence concerns the gene KCNA1 and channelopathy.