Mutations in numerous genes including msh homeobox 1 (MSX1), paired box 9 (PAX9), Wnt family member 10A (WNT10A), axis inhibition protein 2 (AXIN2), ectodysplasin A (EDA), and Wnt family member 10B (WNT10B) have been associated with nonsyndromic oligodontia [2–7]. Here, PAX9 is linked to Oligodontia.