In 2013, the 5th World Symposium on Pulmonary Hypertension established the ENG gene to be a PAH‐associated gene, since two missense PAH‐associated variants (p.G214S [rs150932144] and p.G545S [rs142896669]) were reported (Simonneau et al., 2013). Here, ENG is linked to pulmonary hypertension.