Furthermore, specific VKH disease-associated HLAs including HLA-B54, -DQ4, -DR4, -DR53 and -DRβ1∗04 were negative in this patient.[25,26] Leukocytes in the CSF were almost absent, and was not consistent with VKH disease in the acute phase.[27] The IL-6 level in the aqueous humor of our patient was considerably low compared with that of VKH disease patients.[28] During the clinical course, she recovered promptly under only antihypertensive treatment. Here, HLA-S is linked to Vogt-Koyanagi-Harada disease.