Recently it has become clear that the SDHB‐linked tumour syndrome not only comprises PGLs and phaeochromocytomas, but also non‐paraganglionic tumours such as renal clear cell carcinoma, gastrointestinal stromal tumours (GISTs) and pituitary tumours6, 7, 8, 9, 10, 11, 12. The gene discussed is SDHB; the disease is clear cell renal carcinoma.