6% higher levels of VCAM-1 (1178.3 [815.2–1600.1] vs. 893.8 [635.4–959.8] ng/ml, p = 0.02) and 41% higher thrombomodulin levels (11.3 [7.8–17.6] vs. 5.9 [4.4–9.5] ng/ml, p = 0.01) than the remaining GPA patients. Here, THBD is linked to granulomatosis with polyangiitis.