Interestingly, only 7% (2/30) of plexiform neurofibromas and atypical neurofibromas show aberrant ATRX protein expression (Figure 2), compared to 57% (43/74) of MPNSTs showing aberrant ATRX protein (Figure 3, p < 0.0001, Fisher’s Exact Test). Here, ATRX is linked to plexiform neurofibroma.