Odontoonychodermal dysplasia (OODD) and Schopf–Schulz–Passarge syndrome (SSPS) are autosomal recessive disorders caused by homozygous or compound heterozygous missense mutations in WNT10A (wingless-type MMTV integration site family, member 10A). The gene discussed is WNT10A; the disease is odonto-onycho-dermal dysplasia.