Several point mutations of the KCNA1 gene coding for the Kv1.1 subunit (Browne et al., 1994; reviewed in Ovsepian et al., 2016), have been reported in patients suffering from episodic ataxia type 1 (EA1), an autosomal dominant neurological disease with paroxysmal cerebellar ataxia, epilepsy, myokymia (Browne et al., 1994). This evidence concerns the gene KCNA1 and Myokymia.