Uncommonly it may be found outside the salivary glands and it's especially rare in the nasal cavity.<h4>Case presentation</h4>A 71-year female had complaints of swelling at the base of nose, Fine needle aspiration (FNA) from the swelling revealed features of adenoid cystic carcinoma; cell block & IHC for CD-117 was positive.<h4>Conclusions</h4>Sino-nasal ACC (SNACC) continues to pose diagnostic and therapeutic challenges to clinicians. Here, KIT is linked to adrenal cortex carcinoma.