Loss-of-function mutations in the human ether-á-go-go related (hERG) gene result in a dysfunctional Kv11.1 voltage-gated potassium channel causing delayed cardiac repolarization, and long QT syndrome (LQTS) with increased risk of cardiac arrhythmias and sudden death [1–4]. This evidence concerns the gene KCNH2 and familial long QT syndrome.