ACADS and systemic primary carnitine deficiency disease: There were 11 infants diagnosed with FAO disorders, for a total prevalence rate of 1:9098 (eight cases of primary carnitine deficiency [PCD], two cases of medium-chain acyl-CoA dehydrogenase [MCAD] deficiency, and one case of short-chain acyl-CoA dehydrogenase [SCAD] deficiency) (Table 3).