Other familial potassium channelopathies associated with cerebellar dysfunction include spinocerebellar ataxia type 13 (SCA13), episodic ataxia type 1 (EA1), and sensorineural deafness, ataxia, mental retardation, and electrolyte imbalance (SESAME syndrome) which are caused by mutations in the KCNC3, KCNA1, and KCNJ10 genes, respectively [25–27]. The gene discussed is KCNA1; the disease is cerebellar ataxia.