HNF1B and autosomal dominant medullary cystic kidney disease with or without hyperuricemia: With the recently identified ADTKD-MUC1 subtype (OMIM #174000; originally referred to as MCKD type 1), four genes (UMOD (OMIM #603860, #162000 and #609886; ADTKD-UMOD; MCKD type 2), REN (OMIM #613092; ADTKD-REN), and HNF1B (OMIM #137920; ADTKD-HNF1B)) have so far been repeatedly assigned to the ADTKD-spectrum1,5–8.