The most common types of SCAs worldwide include SCA1, SCA2, SCA3, SCA6, SCA7, and dentatorubral-pallidoluysian atrophy (DRPLA), all caused by unstable trinucleotide repeat Cytosine-Adenine-Guanine (CAG) expansions in the coding region of the respective genes [3, 6]. The gene discussed is ATXN3; the disease is Dentatorubral pallidoluysian atrophy.