BIBD is rare and has been reported in casesdiagnosed clinically as bvFTD, FTD-MND, PSP and PLS/CBS (as well as pureMND).15 The nomenclaturederives from the basophilic cytoplasmic inclusions observed on haematoxylin andeosin staining, which are strongly positive for FUS immunohistochemistry.65 NIIs are rare in BIBD, but GCIsare common. This evidence concerns the gene FUS and frontotemporal dementia.