Characterization of the YG8 and YG8sR models, carrying FXN exogenous genes with 90 + 190 or 200 GAA repeats, respectively, showed age‐dependent FRDA symptoms such as ambulatory difficulties, decreased frataxin mRNA levels, abnormal root ganglia, reduced aconitase activity and oxidative stress 27, 54. The gene discussed is FXN; the disease is Friedreich ataxia.