NF1 or von Recklinghausen’s disease is another autosomal dominant disorder, characterized by neurofibromas, café-au-lait spots, freckling, Lisch nodules, phaeochromocytoma and paraganglioma: 0.1 to 5.7% of patients with the NF1 gene present with solitary and benign phaeochromocytomas (14). This evidence concerns the gene NF1 and pheochromocytoma.