For example, mitochondrial toxins are known to induce Parkinsonism in human and animal models and several genes directly linked to mitochondrial function and mitophagy, including DJ‐1 and PINK1, have strong associations with EOPD.1, 2, 3 Although, the mitochondrial aminoacyl‐tRNA synthetases (mtARSs) are key components of the mitochondrial translation machinery and are associated with disturbances of mitochondria function, they have not yet been associated with PD or Parkinsonian syndromes. Here, PARK7 is linked to Parkinson disease.