Previous studies on mutant mice lacking USH1 proteins—myosin VIIa, harmonin, cadherin‐23, protocadherin‐15 and sans—revealed a fragmentation of hair bundles, initiated at embryonic stages and accounting for the profound deafness and balance phenotypes (Lefèvre et al, 2008; see also Fig 3A). The gene discussed is USH1G; the disease is deafness.