Adrenal PC is more common in VHL disease, whereas (extra-adrenal) PGL with SDHB disease but with a secretory pattern (predominantly noradrenergic) is similar to VHL and SDHX and there are similar features on positron emission tomography computed tomography with tracers such as 18-fluorodeoxyglucose (28). The gene discussed is SDHB; the disease is von Hippel-Lindau disease.