The same applied to the nine patients diagnosed with “atypical Usher syndrome” in whom course and/or age of onset of sensorineural hearing impairment and RP did not allow for clear‐cut assignment to USH1 or USH2 and who had no additional abnormalities: They were found to have atypical expressions of USH1B (MYO7A), USH1D (CDH23), USH2A, and USH2C (ADGRV1). The gene discussed is ADGRV1; the disease is Usher syndrome.