About 70% of TNDM cases are due to abnormalities in the 6q24 region, with the remainder of patients mainly having mutations in the KCNJ11 and ABCC8 genes encoding the Kir6.2 and SUR1 subunits of the pancreatic ATP-sensitive potassium (KATP) channel (10). Here, KCNJ11 is linked to transient neonatal diabetes mellitus.