CNBP and myotonic dystrophy type 1: DM1 is caused by an expanded CTG repeat in the 3′ untranslated region (UTR) of the Dystrophia Myotonica Protein Kinase gene (DMPK) [3–5], while DM2 is caused by expanded CCTG repeats in intron 1 of the CCHC-type zinc finger, Nucleic acid Binding Protein gene (CNBP/ZNF9) [6].