Mutations in MYH7 are a well-known cause of several types of cardiomyopathy, including hypertrophic cardiomyopathy (HCM) [1], dilated cardiomyopathy (DCM) [2], possibly occurring as peripartum cardiomyopathy [3], and left ventricular noncompaction, also referred to as noncompaction cardiomyopathy (NCCM) [4], in addition to skeletal myopathies with or without cardiac involvement [5]. Here, MYH7 is linked to familial dilated cardiomyopathy.