PC/PG, ordinary or composite types, are usually associated with certain hereditary disorders: von Hippel-Lindau syndrome (vHL), multiple endocrine neoplasia syndrome type 2A and 2B (MEN 2A and 2B), NF1 and the recently described familial paraganglioma syndrome [2, 12]. This evidence concerns the gene NF1 and multiple endocrine neoplasia type 2A.